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目前显示的是标签为“Macroglossia”的博文

Anesthetic Management of a Child with Simpson-Golabi-Behmel Syndrome—A Case Report

Read  full  paper  at: http://www.scirp.org/journal/PaperInformation.aspx?PaperID=53797#.VNMmQizQrzE Author(s)   Yoshihiro Morita 1,2,3 , Kyoko Naito 1 , Natsuko Kimoto 2 , Eiji Kimoto 2 , Tetsuji Omata 2 , Nobuo Morita 4 , Masashi Nakagawa 1*   Affiliation(s) 1 Department of Anesthesiology, Kinan Hospital, Tanabe, Japan . 2 Department of Oral and Maxillofacial Surgery, Kinan Hospital, Tanabe, Japan . 3 Department of Oral and Maxillofacial Surgery, Seichokai Hannan Municipal Hospital, Han-nan, Japan . 4 Department of Oral and Maxillofacial Surgery, NS Medical & Healthcare Service General Incorporation Foundation, Wakayama, Japan . ABSTRACT Simpson-Golabi-Behmel syndrome (SGBS) is an X-linked recessive condition associated with pre-natal and postnatal overgrowth with visceral and skeletal anomalies. Abnormal airway anatomy may complicate the perioperative management of SGBS. However, there have been few reports regarding the an...